Bieniasz Jolanta, Maj Anna, Noczyńska Anna
Klinika Endokrynologii i Diabetologii Wieku Rozwojowego AM we Wrocławiu, Wrocław.
Endokrynol Diabetol Chor Przemiany Materii Wieku Rozw. 2006;12(1):69-72.
Fibrous dysplasia of bone is a rare congenital bone disease, usually coming out before the age of 30. It is 2.5% of all bone tumours and 7.5 % of benign tumours of bones. The authors present a case of a 12-years old girl with fibrous dysplasia of bone admitted to the Department with hyperparathyroidism suspicion. Pathological changes were localized in the orbital cavity and sinuses. The diagnosis was established on the basis of the clinical course, imaging and histopathological examinations. The therapy with pamidronian acid was applied.
骨纤维发育不良是一种罕见的先天性骨病,通常在30岁之前发病。它占所有骨肿瘤的2.5%,占骨良性肿瘤的7.5%。作者报告了一例12岁患骨纤维发育不良的女孩,因疑似甲状旁腺功能亢进入住该科室。病变位于眼眶和鼻窦。根据临床病程、影像学和组织病理学检查确诊。采用了帕米膦酸治疗。