原发性肾血管肉瘤：一种罕见的恶性肿瘤。病例报告及文献复习

Primary renal angiosarcoma: a rare malignancy. A case report and review of the literature.

作者信息

Leggio Lorenzo, Addolorato Giovanni, Abenavoli Ludovico, Ferrulli Anna, D'Angelo Christina, Mirijello Antonio, Vonghia Luisa, Schinzari Giovanni, Arena Vincenzo, Perrone Luca, Citterio Franco, Bonomo Lorenzo, Rapaccini Gian Ludovico, Capelli Arnaldo, Barone Carlo, Gasbarrini Giovanni

机构信息

Institute of Internal Medicine, Catholic University of Rome, Rome, Italy.

出版信息

Urol Oncol. 2006 Jul-Aug;24(4):307-12. doi: 10.1016/j.urolonc.2005.10.002.

DOI:10.1016/j.urolonc.2005.10.002

PMID:16818182

Abstract

Angiosarcoma is a rare malignant tumor occurring in less than 2% of soft tissue sarcomas. Angiosarcoma involving the kidney usually represents metastasis from skin or visceral primary lesions, while angiosarcoma primarily occurring in the kidney is a very rare neoplasm. In the English literature, from 1942 to the present, only 19 cases of primary kidney angiosarcoma have been reported. A case of primary renal angiosarcoma presenting as a large kidney mass and flank pain occurring after traumatism is reported. The present case represents further evidence of a rare malignancy.

摘要

血管肉瘤是一种罕见的恶性肿瘤，在软组织肉瘤中所占比例不到2%。累及肾脏的血管肉瘤通常代表皮肤或内脏原发性病变的转移，而主要发生在肾脏的血管肉瘤是一种非常罕见的肿瘤。在英文文献中，从1942年至今，仅报道了19例原发性肾血管肉瘤。本文报道了1例原发性肾血管肉瘤病例，表现为外伤后出现的巨大肾脏肿块和侧腹痛。本病例进一步证明了这种罕见恶性肿瘤的存在。