Foguem C, Launay D, Lambert M, Quemeneur T, Hachulla E, Wallaert B, Hatron P-Y
Service de médecine interne, hôpital Claude-Huriez, CHRU de Lille, 59037 Lille, France.
Rev Med Interne. 2006 Aug;27(8):620-4. doi: 10.1016/j.revmed.2006.04.011. Epub 2006 Jun 5.
Cystic lung disease is characterised on chest iconography by foci of decreased lung density with definable and thinned walls (wall thickness<4 mm) and with length's diameter superior at 1 cm. Cystic lung disease is exceptionally associated with the Sjögren's syndrome; very few cases have been described.
We report two cases of cystic lung disease associated with Sjögren's syndrome, one occurring in a Lupus-Sjögren's overlapping syndrome, and another revealing primary Sjögren's syndrome.
The Sjögren's syndrome should be recognised as could be associated with Cystic lung disease; and latent Sjögren's syndrome should be researched in presence of cystic lung lesions.
肺囊性疾病在胸部影像学上的特征为肺密度降低区域,伴有可明确界定且变薄的壁(壁厚<4毫米),长径大于1厘米。肺囊性疾病极少与干燥综合征相关;仅有极少数病例被报道。
我们报告两例与干燥综合征相关的肺囊性疾病病例,一例发生于狼疮-干燥综合征重叠综合征,另一例为原发性干燥综合征的首发表现。
干燥综合征应被视为可能与肺囊性疾病相关;在出现肺囊性病变时应排查潜在的干燥综合征。