Yano Shunsuke, Hida Kazutoshi, Nagashima Kazuo, Iwasaki Yoshinobu
Department of Neurosurgery, University of Hokkaido, Graduate School of Medicine, Sapporo, Japan.
Neurosurgery. 2004 Sep;55(3):712. doi: 10.1227/01.neu.0000134614.73236.a4.
Fibrous hamartoma of infancy (FHI) in the spinal cord is very rare. It is characterized histopathologically by three elements: fibrous, adipose, and myxoid mesenchymal tissues.
A 10-month-old boy presented with paraparesis. Magnetic resonance imaging showed a large intradural mass that occupied the space between the T10 and L4 levels.
We performed partial removal of the mass. Histopathological examination of the lesion revealed that it was composed of collagen bundles and fibrous tissue interspersed with adipose tissue, mesenchymal tissue, and glial tissue, and it was diagnosed as FHI.
FHI in the central nervous system, especially in the spine, is very rare, and the presence of glial tissue admixed with particular components of FHI is quite exceptional.
脊髓内的婴儿纤维性错构瘤（FHI）非常罕见。其组织病理学特征为包含三种成分：纤维组织、脂肪组织和黏液样间充质组织。
一名10个月大的男童出现双下肢轻瘫。磁共振成像显示一个巨大的硬膜内肿块，占据了T10至L4水平之间的空间。
我们对肿块进行了部分切除。病变的组织病理学检查显示，其由胶原束和纤维组织组成，其间散在脂肪组织、间充质组织和神经胶质组织，诊断为FHI。
中枢神经系统，尤其是脊柱中的FHI非常罕见，且神经胶质组织与FHI的特定成分混合存在的情况相当特殊。
