Cho Judy H, Abraham Clara
Department of Medicine, Yale University, New Haven, Connecticut 06510, USA.
Annu Rev Med. 2007;58:401-16. doi: 10.1146/annurev.med.58.061705.145024.
The inflammatory bowel diseases (IBD) are comprised of two major subphenotypes, Crohn's disease (CD) and ulcerative colitis (UC). A significant role for genetic factors in IBD was established from epidemiologic studies and, more recently, the identification of well-established disease associations, notably the association of Nod2 (CARD15) polymorphisms with CD. The mapping to CD of Nod2 variants that alter protein function represents one of the earliest, most well-established, associations in complex genetic disorders. Since the initial discovery, genotype-phenotype correlations, definition of Nod2 expression and signaling pathways, association studies in other, related disorders, and features of Nod2 deficiency in murine models have been reported. Taken together, the Nod2 association to CD provides an illustrative model of the role of single gene variants in disease pathogenesis for common, complex multigenic disorders. Here we review general aspects of IBD genetics with particular focus on the role of Nod2 in CD.
炎症性肠病(IBD)由两种主要亚型组成,即克罗恩病(CD)和溃疡性结肠炎(UC)。流行病学研究确立了遗传因素在IBD中的重要作用,最近又发现了一些明确的疾病关联,尤其是Nod2(CARD15)多态性与CD的关联。改变蛋白质功能的Nod2变体与CD的定位关联是复杂遗传疾病中最早、最明确的关联之一。自最初发现以来,已报道了基因型-表型相关性、Nod2表达和信号通路的定义、其他相关疾病的关联研究以及小鼠模型中Nod2缺陷的特征。总体而言,Nod2与CD的关联为单基因变体在常见复杂多基因疾病发病机制中的作用提供了一个典型模型。在此,我们综述IBD遗传学的一般方面,特别关注Nod2在CD中的作用。