Kocyła-Karczmarewicz Beata, Klimczak-Slaczka Dorota, Grałek Mirosława, Chipczyńska Barbara
Kliniki Okulistyki Instytutu Pomnik, Centrum Zdrowia Dziecka w Warszawie.
Klin Oczna. 2006;108(4-6):180-3.
Sturge-Weber syndrome is a rare congenital neurooculocutaneous disorder. Ocular involvement can include glaucoma and vascular malformations of the conjunctiva, episclera, choroid and retina.
16 children (16 eyes) with Sturge-Weber syndrome associated with glaucoma (mean age--34 month, mean follow up 8.87 years) treated in our institution, were reviewed. In retrospective analysis were assessed: IOP and postoperative complications after diode laser cyklophotocoagulation (16 eyes), after trabeculectomy (6 eyes) and trabeculectomy with MMC (3 eyes).
In ten eyes (62.5%) good result (IOP 6-22 mmHg) post cyclophotokoagulation--(3x) was recorded, as well as in 3 eyes (50%) post trabeculectomy and in 3 eyes (100%) post trabeculectomy with MMC 0.2/4 min. No postoperative complications occured in cyclophotocoagulation group. Complications after trabeculectomy were the following: 3 cases of hypotony, 4 cases with shallow anterior chamber and 5 with choroidal effusions.
Diode laser cyclophotocoagulation combined with topical medication is an effective and safe treatment of glaucoma in children with Sturge-Weber syndrome.
斯特奇-韦伯综合征是一种罕见的先天性神经眼皮肤疾病。眼部受累可包括青光眼以及结膜、巩膜表层、脉络膜和视网膜的血管畸形。
回顾性分析了在我们机构接受治疗的16例患有与青光眼相关的斯特奇-韦伯综合征的儿童（16只眼）（平均年龄34个月，平均随访8.87年）。评估了以下内容：二极管激光睫状体光凝术后（16只眼）、小梁切除术后（6只眼）以及小梁切除术联合丝裂霉素C术后（3只眼）的眼压和术后并发症。
10只眼（62.5%）在进行3次睫状体光凝术后取得了良好效果（眼压6 - 22 mmHg），3只眼（50%）在小梁切除术后取得良好效果，3只眼（100%）在小梁切除术联合0.2/4分钟丝裂霉素C术后取得良好效果。睫状体光凝组未发生术后并发症。小梁切除术后的并发症如下：3例低眼压、4例前房浅和5例脉络膜渗漏。
二极管激光睫状体光凝联合局部用药是治疗斯特奇-韦伯综合征患儿青光眼的一种有效且安全的方法。
