Di Scioscio V, Zompatori M, Mistura I, Montanari P, Santilli L, Luccaroni R, Sverzellati N
Department of Radiology, S Orsola-Malpighi Policlinic, Medical University of Bologna, Bologna, Italy.
Acta Radiol. 2006 Oct;47(8):798-800. doi: 10.1080/02841850600849084.
Williams-Campbell syndrome is a cystic bronchiectatic disease secondary to deficiency or defect of cartilaginous plates in the wall of the airways. In the literature, two main forms are suggested: congenital and acquired (post-infectious). The most frequent symptoms are represented by recurrent pulmonary infections from childhood. Multislice spiral dynamic CT has a major role in the study of cystic pulmonary disease and in differentiating Williams-Campbell syndrome from the other causes of cystic bronchiectasis, in which even lung function tests can give deceptive results.
威廉姆斯-坎贝尔综合征是一种气道壁软骨板缺乏或缺陷继发的囊性支气管扩张疾病。文献中提出了两种主要形式：先天性和后天性（感染后）。最常见的症状是儿童期反复肺部感染。多层螺旋动态CT在囊性肺病的研究以及将威廉姆斯-坎贝尔综合征与其他导致囊性支气管扩张的原因相鉴别方面发挥着重要作用，在其他原因导致的囊性支气管扩张中，即使肺功能检查也可能给出误导性结果。
