Sharp recanalization of a short esophageal occluding stricture in a patient with epidermolysis bullosa.

BACKGROUND

Although esophageal strictures caused by epidermolysis bullosa are often treated with balloon dilations, complete obstruction has few effective therapies except esophagectomy with colonic replacement.

OBJECTIVE

Resolution of esophageal obstructive lesion without surgical intervention.

DESIGN

Case study.

SETTING

Interventional radiology.

PATIENT

Epidermolysis bullosa with esophageal stricture.

INTERVENTION

Endoscopic- and guidewire-guided sharp recanalization.

MAIN OUTCOME MEASUREMENT

Radiologic evidence of stricture resolution.

RESULTS

Successful recanalization.

LIMITATIONS

Experience of operators (anesthesiologist, endoscopist, interventional radiologist).

CONCLUSIONS

Sharp recanalization of a complete stricture in patients with epidermolysis bullosa is feasible in a controlled setting.