Danon F, Mihaesco C, Bouvry M, Clerc M, Seligmann M
Scand J Haematol. 1975 Aug;15(1):5-9. doi: 10.1111/j.1600-0609.1975.tb01048.x.
The tenth case of mu chain disease is described. The patient lives in Ivory Coast as in our previously reported case. He was not affected with chronic lymphocytic leukaemia and the main clinical feature was liver cirrhosis of unknown origin. The amount of abnormal protein in the serum was great enough to give an abnormal bond on the routine electrophoresis. The protein was devoid of light chains and was present in the form of disulfide linked polymers of incomplete mu chain. The molecular weight of the monomer was approximately 58,000. The protein comprised the Fc fragment and a part of the Fd segment. Bence Jones protein was not found in the urine.
本文描述了第10例μ链病。该患者与我们之前报道的病例一样生活在象牙海岸。他未患慢性淋巴细胞白血病，主要临床特征是不明原因的肝硬化。血清中异常蛋白的量足以在常规电泳上产生异常条带。该蛋白不含轻链，以不完全μ链的二硫键连接聚合物形式存在。单体的分子量约为58,000。该蛋白包含Fc片段和一部分Fd段。尿中未发现本-周蛋白。
