Tévar Elena, Torrelo Antonio, Contreras Félix, Colmenero Isabel, Zambrano Antonio
Servicio de Dermatología, Hospital del Niño Jesús, Madrid, España.
Actas Dermosifiliogr. 2006 Oct;97(8):518-21. doi: 10.1016/s0001-7310(06)73454-8.
We present a patient with phacomatosis pigmentokeratotica (PPK) who developed several basal cell carcinomas on epidermal nevus lesions in adult life. PPK shows an elevated incidence of development of malignant lesions both on the sebaceous or epidermal nevus component as well as on the nevus spilus one.
我们报告一例色素角化性错构瘤病(PPK)患者,该患者在成年期表皮痣病变上发生了数例基底细胞癌。PPK显示皮脂腺痣或表皮痣成分以及斑痣性错构瘤病成分发生恶性病变的发生率均升高。