Finsterer Josef, Stöllberger Claudia, Feichtinger Hans
Krankenanstalt Rudolfstiftung, Vienna, Austria.
Cardiology. 2007;108(3):161-3. doi: 10.1159/000096600. Epub 2006 Oct 23.
Left ventricular hypertrabeculation (LVHT)/non-compaction is frequently associated with neuromuscular disorders. Recently, LVHT has been detected in a 28-year patient with Duchenne muscular dystrophy. Here, the patho-anatomic findings of this patient are presented, which showed LVHT located within in the apex and the anterior and lateral wall, being the most demanded segments during systole. The septum and the left ventricular outflow tract were not involved. The patho-anatomic specimen also showed aberrant bands and false tendons, a frequent finding in hearts with LVHT. The patho-anatomic findings were in line with those of LVHT patients with or without neuromuscular disorders.
左心室肌小梁增多（LVHT）/心肌致密化不全常与神经肌肉疾病相关。最近，在一名28岁的杜氏肌营养不良患者中检测到LVHT。在此，展示了该患者的病理解剖学发现，结果显示LVHT位于心尖以及前壁和侧壁，这些是收缩期需求最大的节段。室间隔和左心室流出道未受累。病理解剖标本还显示有异常条索和假腱索，这在LVHT患者的心脏中是常见发现。病理解剖学发现与伴有或不伴有神经肌肉疾病的LVHT患者一致。
