Cummings Shelly A, Rubin David T
Cancer Risk Clinic, The University of Chicago, Section of Hematology/Oncology, 5841 South Maryland Avenue, MC 2115, Chicago, IL 60637, USA.
J Genet Couns. 2006 Dec;15(6):465-76. doi: 10.1007/s10897-006-9057-0.
Inflammatory bowel disease (IBD) is an umbrella term referring to two chronic idiopathic intestinal diseases: ulcerative colitis (UC) and Crohn's disease (CD). Both UC and CD are characterized by immune activation that leads to symptoms, but the location, severity and behavior of the inflammation varies among individuals and in characteristic ways between UC and CD. A majority of patients with IBD are diagnosed in young adulthood, but the response to therapy is variable and difficult to predict, with some patients demonstrating a prompt and effective remission while others have continuous symptoms that do not respond to existing medical options. Surgery remains a frequent and necessary occurrence among patients with IBD, but in UC it is considered curative, while in CD only temporizing. Clinical observations, epidemiological studies, and molecular genetics have provided strong evidence that both genetic and environmental factors are important determinants for disease susceptibility. In recent years, a number of genes have been identified that associate with CD and UC, although the clinical utility of these discoveries in patients or in susceptible family members has not been determined. Nonetheless, it is hoped that these fundamental advances in our understanding of IBD will lead to better therapies for patients and prevention strategies for those who are susceptible. Effective incorporation of clinical genetic testing for IBD into practice will require appropriate education and counseling.
炎症性肠病(IBD)是一个统称,指两种慢性特发性肠道疾病:溃疡性结肠炎(UC)和克罗恩病(CD)。UC和CD均以导致症状的免疫激活为特征,但炎症的部位、严重程度和表现因人而异,且在UC和CD之间存在特征性差异。大多数IBD患者在年轻成年期被诊断出来,但对治疗的反应各不相同且难以预测,一些患者能迅速有效缓解,而另一些患者则持续出现症状,对现有医疗手段无反应。手术在IBD患者中仍然很常见且必要,但在UC中被认为是治愈性的,而在CD中只是临时性的。临床观察、流行病学研究和分子遗传学提供了强有力的证据,表明遗传和环境因素都是疾病易感性的重要决定因素。近年来,已经确定了一些与CD和UC相关的基因,尽管这些发现对患者或易感家庭成员的临床实用性尚未确定。尽管如此,人们希望我们在IBD理解上的这些根本性进展将为患者带来更好的治疗方法,并为易感人群带来预防策略。将IBD临床基因检测有效地纳入实践将需要适当的教育和咨询。