Erer Sevda, Boz Meral, Taskapilioglu Ozlem, Hakyemez Bahattin, Kaderli Berkant, Zarifoglu Mehmet
Uludag University Medical Faculty Department of Neurology, Gorukle / Nilufer 16059, Bursa, Turkey.
J Neurol Sci. 2006 Dec 21;251(1-2):134-7. doi: 10.1016/j.jns.2006.09.015. Epub 2006 Nov 15.
Susac's syndrome is a vasospastic disease resulting from bilateral microangiopathy of the brain, cochlea and retina. It is characterized by encephalopathy, bilateral sensorineural fluctuating hearing loss and visual loss. It is very uncommon and usually affects women during young adulthood. Since all three symptoms of the triad may not be present, the clinical diagnosis is difficult. Therefore, neuroimaging, particularly magnetic resonance imaging, has an important role in establishing the diagnosis. In this case report, we present a young woman who had all the symptoms of Susac's syndrome. This is the first Susac's syndrome case reported in Turkey.
苏萨克综合征是一种由脑、耳蜗和视网膜双侧微血管病变引起的血管痉挛性疾病。其特征为脑病、双侧感音神经性波动性听力损失和视力丧失。该病非常罕见,通常在青年期影响女性。由于三联征的所有三种症状可能并不都出现,临床诊断困难。因此,神经影像学检查,尤其是磁共振成像,在确立诊断方面具有重要作用。在本病例报告中,我们介绍了一名具有苏萨克综合征所有症状的年轻女性。这是土耳其报道的首例苏萨克综合征病例。