Yoshimura Naoki, Murakami Hirohisa, Otaka Shingo, Watanabe Kazuhiro, Watanabe Sayaka, Uese Keiichiro, Nomura Keiko, Hashimoto Ikuo, Kanegane Hirokazu, Ichida Fukiko, Misaki Takuro
First Department of Surgery, Toyama University School of Medicine, Toyama University, Toyama, Japan.
Circ J. 2006 Dec;70(12):1655-7. doi: 10.1253/circj.70.1655.
An 18-month-old girl with hereditary spherocytosis underwent closure of the ventricular septal defect, commissurotomy of the pulmonary valve, and patch angioplasty of the pulmonary trunk without previous splenectomy. No serious complications as a result of hemolysis occurred in the perioperative period. Open heart surgery can therefore be safely performed in young children with congenital heart disease and hereditary spherocytosis who have not previously undergone splenectomy.
一名患有遗传性球形红细胞增多症的18个月大女孩,在未预先进行脾切除术的情况下接受了室间隔缺损修补术、肺动脉瓣交界切开术和肺动脉干补片血管成形术。围手术期未发生因溶血导致的严重并发症。因此,对于患有先天性心脏病且未预先进行脾切除术的遗传性球形红细胞增多症幼儿,可以安全地进行心脏直视手术。