一例遗传性球形红细胞增多症患儿在先天性心脏手术中成功实施换血疗法。
The Successful Use of an Exchange Transfusion in a Child with Hereditary Spherocytosis Undergoing Congenital Cardiac Surgery.
机构信息
Oklahoma Children's Hospital at OU Health, Oklahoma City, Oklahoma.
出版信息
J Extra Corpor Technol. 2021 Jun;53(2):137-139. doi: 10.1182/ject-2000060.
Abstract
Little is reported in the literature regarding hereditary spherocytosis (HS) and cardiopulmonary bypass (CPB). We present a case of a 19-month-old girl child who was referred for an atrioventricular septal defect (AVSD) and HS. The patient underwent surgical repair, and an exchange transfusion was performed at the initiation of CPB. No significant hemolysis or events attributed to HS were observed during or after CPB. The surgical repair of an AVSD in a pediatric patient with HS and total volume exchange transfusion is herein reported.
摘要
关于遗传性球形红细胞增多症（HS）和体外循环（CPB），文献报道甚少。我们报告了一例 19 个月大的女孩，因房间隔和室间隔缺损（AVSD）和 HS 而转诊。患者接受了手术修复，在 CPB 开始时进行了换血。在 CPB 过程中和之后，没有观察到明显的溶血或归因于 HS 的事件。本文报告了一例 HS 合并全血容量换血的小儿患者的 AVSD 手术修复。
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引用本文的文献
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本文引用的文献
1
A de novo ANK1 mutation associated to hereditary spherocytosis: a case report.
BMC Pediatr. 2019 Feb 18;19(1):62. doi: 10.1186/s12887-019-1436-4.
3
Open-heart surgery using a centrifugal pump: a case of hereditary spherocytosis.
J Cardiothorac Surg. 2016 Aug 26;11(1):138. doi: 10.1186/s13019-016-0534-8.
4
Perioperative considerations in a sickle cell patient undergoing cardiopulmonary bypass.
Indian J Anaesth. 2014 May;58(3):319-22. doi: 10.4103/0019-5049.135047.
5
Hereditary spherocytosis.
Lancet. 2008 Oct 18;372(9647):1411-26. doi: 10.1016/S0140-6736(08)61588-3.
6
Open heart operation in a child with congenital heart disease and hereditary spherocytosis.
Circ J. 2006 Dec;70(12):1655-7. doi: 10.1253/circj.70.1655.
7
Open heart operation in a patient with hereditary spherocytosis: a case report.
Ann Thorac Cardiovasc Surg. 2001 Dec;7(6):375-7.
8
[Anatomic correction of double-outlet right ventricle associated with hereditary spherocytosis--a case report].
Nihon Kyobu Geka Gakkai Zasshi. 1996 Dec;44(12):2164-71.
9
Open heart surgery in presence of hereditary spherocytosis.
J Cardiovasc Surg (Torino). 1995 Oct;36(5):447-8.
10
Open heart operation in a young child with spherocytosis.
Ann Thorac Surg. 1994 Oct;58(4):1166-8. doi: 10.1016/0003-4975(94)90481-2.
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