一例脊索分裂综合征：一名患有神经肠瘘并伴有脑膜炎的儿童。

A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis.

作者信息

van Ramshorst Gabrielle H, Lequin Maarten H, Mancini Grazia M S, van de Ven Cornelis P

机构信息

Department of Pediatric Surgery, Erasmus Medical Center/Sophia Children's Hospital, 3000 CB Rotterdam, the Netherlands.

出版信息

J Pediatr Surg. 2006 Dec;41(12):e19-23. doi: 10.1016/j.jpedsurg.2006.09.070.

DOI:10.1016/j.jpedsurg.2006.09.070

PMID:17161173

Abstract

The authors describe a case of split notochord syndrome with a neuroenteric fistula in a newborn presenting with meningitis. Associated anomalies included agenesis of the corpus callosum, short colon, malrotation, epispadias, and an abnormally high bifurcation of the abdominal aorta and inferior vena cava. The embryological mechanisms and etiologic theories are discussed in short.

摘要

作者描述了一例患有神经肠瘘的新生儿脊索分裂综合征，该新生儿伴有脑膜炎。相关畸形包括胼胝体发育不全、短结肠、肠旋转不良、尿道上裂以及腹主动脉和下腔静脉异常高位分叉。简要讨论了胚胎学机制和病因学理论。