Akgür F M, Ozdemir T, Olguner M, Erbayraktar S, Ozer E, Aktuğ T
Department of Pediatric Surgery, Dokuz Eylül University, Medical Faculty, Izmir, Turkey.
J Pediatr Surg. 1998 Aug;33(8):1317-9. doi: 10.1016/s0022-3468(98)90179-8.
Like umblical enteric remnants (eg, umblical sinus and omphalomesenteric fistula), enteric remnants can be seen on the dorsal aspect of the body (dorsal enteric sinus, dorsal enteric fistula IDEF], dorsal enteric diverticulum) in conjunction with complete cleft of the vertebral column. Complete cleft of the vertebral column associated with gastrointestinal tract and central nervous system anomalies is known as "split notochord syndrome" (SNS). The authors present an unreported variant of SNS having dorsal enteric diverticulum adjacent to the DEF. The patient died 17 days after surgical repair.
与脐部肠道残余物（如脐窦和脐肠系膜瘘）一样，肠道残余物可见于身体背侧（背侧肠道窦、背侧肠道瘘[IDEF]、背侧肠道憩室），并伴有脊柱完全裂开。与胃肠道和中枢神经系统异常相关的脊柱完全裂开被称为“分裂脊索综合征”（SNS）。作者报告了一种未被报道的SNS变异型，其背侧肠道憩室毗邻背侧肠道瘘。患者在手术修复后17天死亡。
