表现为视神经脊髓炎的原发性干燥综合征

Primary Sjögrens syndrome presenting as neuromyelitis optica.

作者信息

Gökçay Figen, Celebisoy Neşe, Gökçay Ahmet, Kabasakal Yasemin, Oder Gonca

机构信息

Department of Neurology, Ege University Medical School, Bornova, Izmir, Turkey.

出版信息

Pediatr Neurol. 2007 Jan;36(1):58-60. doi: 10.1016/j.pediatrneurol.2006.07.008.

DOI:10.1016/j.pediatrneurol.2006.07.008

PMID:17162200

Abstract

This report presents a patient with Devics neuromyelitis optica associated with primary Sjögrens syndrome. Her first attack was right-sided optic neuritis at age 10 years. Attacks involving both optic nerves and medulla spinalis were recorded during the ensuing years. The diagnosis of Sjögrens syndrome could not be made until the second decade because it was not suspected.

摘要

本报告介绍了一名患有与原发性干燥综合征相关的视神经脊髓炎谱系疾病（Devic's病）的患者。她的首次发作是在10岁时出现右侧视神经炎。在随后的几年里记录到了累及双侧视神经和脊髓的发作。由于未被怀疑，直到第二个十年才确诊干燥综合征。