Wiegand J, Neid M, Kaiser T, Wittekind C, Mössner J, Tillmann H L, Schiefke I
Universitätsklinikum Leipzig, Medizinische Klinik und Poliklinik II, Leipzig, Germany.
Z Gastroenterol. 2006 Dec;44(12):1227-9. doi: 10.1055/s-2006-927137.
In contrast to Asia, autoimmune pancreatitis is rare in the Western population. The present case report describes the coexistence of primary biliary cirrhosis and autoimmune pancreatitis accompanied by sclerosing cholangitis of the intrahepatic bile ducts and the hilar region. It is important to differentiate sclerosing cholangitis due to autoimmune pancreatitis from primary sclerosing cholangitis and primary biliary cirrhosis, because the former responds to steroids, while the latter do not. The article highlights important diagnostic difficulties and suggests racial differences between Caucasian and Asian patients.
与亚洲不同，自身免疫性胰腺炎在西方人群中较为罕见。本病例报告描述了原发性胆汁性肝硬化与自身免疫性胰腺炎并存，并伴有肝内胆管和肝门区硬化性胆管炎。将自身免疫性胰腺炎所致的硬化性胆管炎与原发性硬化性胆管炎和原发性胆汁性肝硬化区分开来很重要，因为前者对类固醇有反应，而后者则无。本文强调了重要的诊断难点，并提示白种人和亚洲患者之间存在种族差异。
