Kanamori Yutaka, Hashizume Kohei, Sugiyama Masahiko, Tomonaga Tetsuya, Takayasu Hajime, Ishimaru Tetsuya, Terawaki Kan, Suzuki Kan, Goishi Keiji, Takamizawa Masaru
Department of Pediatric Surgery, The University of Tokyo Hospital, 7-3-1 Hongo, Tokyo 113-8655, Japan.
Surg Today. 2007;37(1):30-3. doi: 10.1007/s00595-006-3324-4. Epub 2007 Jan 1.
Body stalk anomaly is characterized by severe scoliosis, severe pulmonary hypoplasia, and giant omphalocele. The prognosis of the disease is poor and most obstetricians consider it fatal. Very few patients with body stalk anomaly survive. We report the case of a baby diagnosed with body stalk anomaly in fetal life, who was saved by intensive care after birth. We closed the giant omphalocele successfully by placing karaya gum sheets over it, which created a humidified environment and promoted natural skin epithelization over the skin defect.
躯体蒂异常的特征为严重脊柱侧弯、严重肺发育不全和巨大脐膨出。该病预后较差，大多数产科医生认为其为致命性疾病。极少有躯体蒂异常的患者存活。我们报告一例在胎儿期被诊断为躯体蒂异常的婴儿病例，其出生后经重症监护得以挽救。我们通过在巨大脐膨出上覆盖卡拉亚树胶水片成功将其闭合，该片创造了一个湿润的环境并促进了皮肤缺损处的自然皮肤上皮化。
