Acute para-esophageal hernia in Ehlers-Danlos Syndrome.

Para-esophageal herniation is a recognized complication of the Ehlers-Danlos syndrome. While chronic herniation is well described, acute symptomatic herniation is far less common. We describe a case of acute, life-threatening para-esophageal herniation of the abdominal viscera in a young woman with Ehlers-Danlos syndrome. Careful anaesthetic assessment and surgical management resulted in a successful clinical outcome.