Purohit Neeraj, Marsland Daniel, Roberts Neil, Townsend Edward
Department of Thoracic Surgery, Royal Brompton and Harefield NHS Trust, Hill End Road, Harefield, Middlesex UB9 6JH, UK.
Interact Cardiovasc Thorac Surg. 2009 Jul;9(1):130-1. doi: 10.1510/icvts.2009.204313. Epub 2009 Apr 27.
We present a case of recurrent haemo-pneumothorax in a young female patient with previously undiagnosed Ehlers-Danlos syndrome (EDS). The patient presented with a spontaneous haemo-pneumothorax not associated with menstruation. Following further subsequent episodes, left lower lobectomy was performed. In the past, the patient had suffered recurrent atraumatic bilateral patella dislocations which were never fully investigated. Histology of the lung tissue revealed features suggestive of EDS. Haemothorax is a rare complication of type IV EDS. There are very few reported cases of pulmonary presentation of EDS type IV.
我们报告一例患有此前未确诊的埃勒斯-当洛综合征（EDS）的年轻女性复发性血气胸病例。该患者出现与月经无关的自发性血气胸。在随后又发生几次发作后，进行了左下肺叶切除术。过去，该患者曾反复出现非创伤性双侧髌骨脱位，但从未得到充分检查。肺组织的组织学检查显示有提示EDS的特征。血胸是IV型EDS的一种罕见并发症。关于IV型EDS肺部表现的报道病例非常少。
