Midi I, Dib H, Köseoglu M, Afsar N, Günal D I
Department of Neurology, Marmara University Hospital, Tophanelioglu Cad. No: 13-15, 34640 Altunizade, Istanbul, Turkey.
Neurol Sci. 2006 Dec;27(6):439-41. doi: 10.1007/s10072-006-0727-3.
Chorea is a rare complication of polycythaemia vera. Polycythaemic chorea occurs predominantly in females and usually in generalised form. We present a 66-year-old woman with acute onset hemichorea-ballism with no vascular pathology in the basal ganglia region. A clear relationship was observed between the onset of chorea and worsening of haematological parameters in the patient. After repeated phlebotomies the patient's clinical status was improved. Polycythaemic chorea must be considered, especially in the elderly, as early diagnosis leads to effective treatment and prevention of complications.
舞蹈症是真性红细胞增多症的一种罕见并发症。真性红细胞增多症相关性舞蹈症主要发生于女性,通常为全身性发作。我们报告一名66岁女性,急性起病的偏侧舞蹈症-手足徐动症,基底节区无血管病变。在该患者中观察到舞蹈症发作与血液学参数恶化之间存在明确关联。反复放血治疗后患者的临床状况得到改善。必须考虑真性红细胞增多症相关性舞蹈症,尤其是在老年人中,因为早期诊断可实现有效治疗并预防并发症。