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重度先天性输尿管中段扩张。

Severe congenital midureteral dilatation.

作者信息

Prieto Juan C, Castellan Miguel, Gosalbez Rafael, Labbie Andrew, Perez-Brayfield Marcos

机构信息

Division of Pediatric Urology, Department of Urology, Miami Children Hospital and Jackson Memorial Hospital, University of Miami, Miami, FL 33155, USA.

出版信息

J Pediatr Surg. 2007 Jan;42(1):257-8. doi: 10.1016/j.jpedsurg.2006.09.063.

DOI:10.1016/j.jpedsurg.2006.09.063
PMID:17208577
Abstract

Congenital midureteral stricture is an uncommon cause of prenatal hydronephrosis, and it is generally associated with proximal hydroureteronephrosis . We report a unique case of a congenital severe midureteral dilatation associated with mild proximal ureteral dilatation and normal distal ureteral diameter. The dilated midureter was excised, and an open end-to-end ureteroureterostomy was performed. Follow-up 6 months after surgical correction revealed marked improvement in the left-sided hydronephrosis and complete resolution of the hydroureter.

摘要

先天性中段输尿管狭窄是产前肾积水的罕见原因,通常与近端输尿管肾盂积水有关。我们报告了一例独特的病例,该病例为先天性严重中段输尿管扩张,伴有轻度近端输尿管扩张且远端输尿管直径正常。切除扩张的中段输尿管,并进行了开放式端端输尿管输尿管吻合术。手术矫正6个月后的随访显示,左侧肾积水有明显改善,输尿管积水完全消退。

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引用本文的文献

1
Congenital mid-ureteral stricture: a case report of two patients.先天性输尿管中段狭窄:两例报告。
BMC Urol. 2018 Nov 26;18(1):108. doi: 10.1186/s12894-018-0423-7.