Velchuru Vamsi R, Satish Sandesh G, Guruswamy Raman, Sturzaker Hugh G
Department of Surgery, James Paget Healthcare NHS Trust, Great Yarmouth, United Kingdom.
Breast J. 2007 Jan-Feb;13(1):83-4. doi: 10.1111/j.1524-4741.2006.00368.x.
Von Recklinhausen's neurofibromatosis is an autosomal dominant condition occurring typically with café au lait patches, axillary freckling, multiple fibromata, and Lisch nodules. We present a case of a 36-year-old female who presented with severe neurofibromatosis involving the lower half of the breast. The patient was not keen on mastectomy and pedicle flap reconstruction. A modified wise pattern incision was employed to remove the lower half of the breast and neurofibromatosis leading to a reasonable result.
冯·雷克林豪森神经纤维瘤病是一种常染色体显性疾病,通常表现为牛奶咖啡斑、腋窝雀斑、多发纤维瘤和虹膜错构瘤。我们报告一例36岁女性,其患有累及乳房下半部的严重神经纤维瘤病。患者不愿接受乳房切除术和带蒂皮瓣重建术。采用改良的 Wise 模式切口切除乳房下半部及神经纤维瘤病,取得了合理的效果。