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[巴特综合征——严重羊水过多的罕见病因]

[Bartter syndrome--a rare cause of severe polyhydramnios].

作者信息

Media Jean, Hoseth Gerd Eva

机构信息

Viborg Sygehus, Kvindeafdeling Y, Viborg.

出版信息

Ugeskr Laeger. 2006 Dec 11;168(50):4425-6.

Abstract

We report a case of a 25-year-old woman, gravida II, Para I, in pregnancy week 26 + 4 with severe polyhydramnios. The amniotic fluid index was about 39. Type 2 scanning showed a large urinary bladder only. Treated in pregnancy with repeated aminodrinage, total 21 litres. In week 33 + 5, a Caesarean section was performed. A girl with Apgar score 10/1, 0/10 was born, weight 1,804 grammes. Immediately after birth the child developed polyuria with diuresis, about 8-10 ml/kg/hour, electrolyte disturbance, and vomiting, treated with Losec, Gaviscon, indometacin, and Vioxx. The diagnosis was Bartter syndrome.

摘要

我们报告一例25岁女性病例,孕2产1,孕26 + 4周,患有严重羊水过多。羊水指数约为39。二维超声扫描仅显示一个大膀胱。孕期反复行羊膜腔穿刺引流治疗,总量达21升。孕33 + 5周时行剖宫产。娩出一名女婴,阿氏评分10/1、0/10,体重1804克。出生后立即出现多尿伴利尿,约8 - 10毫升/千克/小时,电解质紊乱及呕吐,采用洛赛克、胃喜康、消炎痛和万络治疗。诊断为巴特综合征。

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