Enjolras O, Riche M C, Merland J J
Service de Neuroradiologie, Hôpital Lariboisière, Paris.
Ann Chir Plast Esthet. 1991;36(4):271-8.
A simple and precise classification has been established during a ten-year international cooperation. There are two major groups: hemangiomas, always regressive; and vascular malformations, which never regress; they grow, throughout life, to varying degrees. Management of vascular malformations has been clearly defined. Capillary malformations do not require examination, unless they are associated with other anomalies, such as hypertrophic underlying bone, or the leptomeningeal vascular anomaly of the Sturge-Weber syndrome. Venous type malformations are diffuse, and consist of entirely anomalous channels, with low flow. CT scan and MRI clearly demonstrate the extent of tissue involvement in venous malformations; for these slow-flow malformations the evaluation is performed without resorting to invasive diagnostic techniques: phlebography is rarely performed, and arteriography is unnecessary. Arteriovenous malformations are dangerous high-flow vascular malformations, leading to skin ischemic necrosis, and congestive cardiac failure. Arteriography shows enlarged tortuous arteries, with arteriovenous shunting, and early venous drainage. CT scan and MRI show the deep components of the lesions. Doppler ultrasound evaluation is used to follow the course of the disease.
在一项为期十年的国际合作中建立了一种简单而精确的分类方法。主要有两大类:血管瘤,通常会自行消退;血管畸形,从不消退,它们在整个生命周期中会不同程度地生长。血管畸形的治疗方法已明确界定。毛细血管畸形一般无需检查,除非与其他异常情况相关,如潜在骨骼肥厚,或患有斯-韦综合征的软脑膜血管畸形。静脉型畸形呈弥漫性,由完全异常的低流量通道组成。CT扫描和磁共振成像(MRI)能清晰显示静脉畸形的组织受累范围;对于这些低流量畸形,评估无需借助侵入性诊断技术:很少进行静脉造影,动脉造影也无必要。动静脉畸形是危险的高流量血管畸形,可导致皮肤缺血性坏死和充血性心力衰竭。动脉造影显示动脉增粗、迂曲,存在动静脉分流及早期静脉引流。CT扫描和MRI显示病变的深部成分。多普勒超声评估用于跟踪病情发展。