Cacciapaglia F, Vadacca M, Coppolino G, Buzzulini F, Rigon A, Zennaro D, Zardi E, Afeltra A
Department of Clinical Medicine, University "Campus Bio-Medico" of Rome, Rome, Italy.
Lupus. 2007;16(1):56-8. doi: 10.1177/0961203306072390.
The antiphospholipid syndrome (APS) is an autoimmune disorder, characterized by a wide spectrum of clinical manifestations. Thromboembolic events, with a greater involvement of extremities veins, are the most common features, and obstruction of abdominal vessels are sporadically reported. We present a singular case of a patient with primary APS (PAPS) that developed a spontaneous splenorenal shunt, secondary to a total portal, mesenteric and splenic vein thrombosis. Spontaneous splenorenal shunt, an uncommon circumstance reported in cirrhotic disease, to the best of our knowledge, has not been previously described in PAPS.
抗磷脂综合征（APS）是一种自身免疫性疾病，其临床表现多种多样。血栓栓塞事件是最常见的特征，四肢静脉受累更为常见，腹部血管阻塞也有零星报道。我们报告了一例原发性抗磷脂综合征（PAPS）患者的特殊病例，该患者因门静脉、肠系膜静脉和脾静脉完全血栓形成而出现自发性脾肾分流。自发性脾肾分流在肝硬化疾病中是一种罕见情况，据我们所知，此前在PAPS中尚未有过描述。
