Aviñó J A, España E, Peris-Martínez C, Menezo J L
Servicio de Oftalmología, Hospital Universitario La Fe, Valencia, España.
Arch Soc Esp Oftalmol. 2007 Mar;82(3):179-81. doi: 10.4321/s0365-66912007000300012.
A 25-year-old woman with encephalopathy and sensorineural hearing loss was referred to us in order to confirm Susac syndrome, due to bilateral visual loss. Funduscopic examination revealed peripheral retinal microangiopathy.
Susac syndrome is typically characterized by the clinical triad of encephalopathy, branch retinal artery occlusions, and hearing loss. In our case, ophthalmic findings were atypical. Interrupted vessels and microaneurisms accumulation in the peripheral retina of both eyes were observed.
一名患有脑病和感音神经性听力损失的25岁女性因双眼视力丧失被转诊至我院以确诊Susac综合征。眼底检查发现周边视网膜微血管病变。
Susac综合征的典型特征为脑病、视网膜分支动脉阻塞和听力损失三联征。在我们的病例中，眼科检查结果不典型。观察到双眼周边视网膜血管中断和微动脉瘤聚集。
