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一例疣状表皮发育不良伴非阳光暴露皮肤区域鳞状细胞癌。

A case of epidermodysplasia verruciformis with squamous cell carcinomas on non-sun-exposed areas of skin.

作者信息

Ansarin Habib, Tajziehchi Leila, Shaianfar Nasrin

机构信息

Department of Dermatology, Hazrat-e-Rasoul Hospital, Iran University of Medical Sciences, Tehran, Iran.

出版信息

Arch Iran Med. 2007 Apr;10(2):261-3.

Abstract

Epidermodysplasia verruciformis is an inherited disorder, characterized by multiple plane warts, pityriasis versicolor-like lesions, defects of cell-mediated immunity, and tendency to develop skin malignancies, primarily on sun-exposed areas. In this article, we present a case of epidermodysplasia verruciformis with multiple plane warts, pityriasis versicolor-like lesions, and squamous cell carcinomas on non-sun-exposed areas of skin. After acitretin prescription, significant improvement was found in plane warts, but not in pityriasis versicolor-like lesions.

摘要

疣状表皮发育不良是一种遗传性疾病,其特征为多发性扁平疣、花斑癣样损害、细胞介导免疫缺陷以及主要在暴露于阳光部位发生皮肤恶性肿瘤的倾向。在本文中,我们报告了1例疣状表皮发育不良患者,其在非阳光暴露部位出现多发性扁平疣、花斑癣样损害及鳞状细胞癌。服用阿维A后,扁平疣有显著改善,但花斑癣样损害无改善。

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