Bini Roberta M, Favilli Silvia, Murzi Bruno, Moschetti Riccardo, Santoro Gennaro, Traini Anna M
Division of Paediatric Cardiology, Anna Meyer Hospital, and Department of Heart and Great Vessels, Careggi University Hospital, Florence, Italy.
J Cardiovasc Med (Hagerstown). 2007 Apr;8(4):281-3. doi: 10.2459/01.JCM.0000263488.07339.d2.
An unusual case of severe supravalvular stenosing ring of the left atrium associated with tricuspid valve dysplasia in an adult symptomatic patient affected by congenitally corrected transposition and unrestrictive ventricular septal defect is reported. The stenosis of the systemic atrioventricular valve possibly prevented the development of obstructive pulmonary vascular disease; removal of the membrane, attached to the tricuspid annulus, together with pulmonary banding was carried out. Clinical conditions improved after surgery. The unusual stenotic lesion of the systemic right ventricular inflow allowed conservative surgical palliation in this adult patient.
报道了一例成人有症状患者的罕见病例，该患者患有先天性矫正型大动脉转位和非限制性室间隔缺损，伴有左心房重度瓣上狭窄环及三尖瓣发育异常。体循环房室瓣狭窄可能阻止了阻塞性肺血管疾病的发展；切除附着于三尖瓣环的隔膜并进行了肺动脉环扎术。术后临床状况改善。体循环右心室流入道这种不寻常的狭窄病变使该成年患者能够接受保守性手术姑息治疗。
