Terrettaz Emmanuel, Frey Jean-Georges, Chavaillaz Olivier
Centre valaisan de pneumologie, 3963 Crans-Montana.
Rev Med Suisse. 2007 Feb 21;3(99):470-2, 474-6.
Pneumoblastoma (PB) is a rare, malignant, primary, pulmonary tumour, of young adults. Its discovery is fortuitous in asymptomatic patients. It is a well-delimited, homogeneous lesion in the lung periphery. Histologically, its structure looks like a normal fetal lung. The surgical resection is the treatment of choice. The radiotherapy is an empirical palliative treatment to relieve dyspnea when other treatments failed. The prognosis is bad: 16% survive 5 years and 8% beyond 10 years, all treatments included. Metastases could appear in the liver, the brain and the bone.
肺母细胞瘤（PB）是一种罕见的、恶性的、原发性肺部肿瘤，好发于年轻人。在无症状患者中，其发现往往是偶然的。它是肺周边界限清晰、均匀一致的病变。组织学上，其结构类似正常胎儿肺。手术切除是首选治疗方法。放射治疗是在其他治疗失败时用于缓解呼吸困难的经验性姑息治疗。预后较差：综合所有治疗方法，16%的患者能存活5年，8%的患者能存活超过10年。转移可能出现在肝脏、脑和骨。
