Calzolari Alessia, Oliviero Isabella, Deaglio Silvia, Mariani Gualtiero, Biffoni Mauro, Sposi Nadia Maria, Malavasi Fabio, Peschle Cesare, Testa Ugo
Department of Hematology, Oncology and Molecular Medicine, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy.
Blood Cells Mol Dis. 2007 Jul-Aug;39(1):82-91. doi: 10.1016/j.bcmd.2007.02.003. Epub 2007 Apr 10.
Different proteins ensure the fine control of iron metabolism at the level of various tissues. Among these proteins, it was discovered a second transferrin receptor (TfR2), that seems to play a key role in the regulation of iron homeostasis. Its mutations are responsible for type 3 hemochromatosis (Type 3 HH). Although TfR2 expression in normal tissues was restricted at the level of liver and intestine, we observed that TfR2 was frequently expressed in tumor cell lines. Particularly frequent was its expression in ovarian cancer, colon cancer and glioblastoma cell lines; less frequent was its expression in leukemic and melanoma cell lines. Interestingly, in these tumor cell lines, TfR2 expression was inversely related to that of receptor 1 for transferrin (TfR1). Experiments of in vitro iron loading or iron deprivation provided evidence that TfR2 is modulated in cancer cell lines according to cellular iron levels following two different mechanisms: (i) in some cells, iron loading caused a downmodulation of total TfR2 levels; (ii) in other cell types, iron loading caused a downmodulation of membrane-bound TfR2, without affecting the levels of total cellular TfR2 content. Iron deprivation caused in both conditions an opposite effect compared to iron loading. These observations suggest that TfR2 expression may be altered in human cancers and warrant further studies in primary tumors. Furthermore, our studies indicate that, at least in tumor cells, TfR2 expression is modulated by iron through different biochemical mechanisms, whose molecular basis remains to be determined.
不同的蛋白质确保在各种组织水平上对铁代谢进行精细调控。在这些蛋白质中,发现了第二种转铁蛋白受体(TfR2),它似乎在铁稳态调节中起关键作用。其突变是导致3型血色素沉着症(3型HH)的原因。尽管TfR2在正常组织中的表达局限于肝脏和肠道水平,但我们观察到TfR2在肿瘤细胞系中经常表达。其在卵巢癌、结肠癌和胶质母细胞瘤细胞系中的表达尤为频繁;在白血病和黑色素瘤细胞系中的表达则较少。有趣的是,在这些肿瘤细胞系中,TfR2的表达与转铁蛋白受体1(TfR1)的表达呈负相关。体外铁加载或铁剥夺实验提供了证据,表明TfR2在癌细胞系中根据细胞铁水平通过两种不同机制进行调节:(i)在某些细胞中,铁加载导致总TfR2水平下调;(ii)在其他细胞类型中,铁加载导致膜结合TfR2下调,而不影响细胞总TfR2含量水平。与铁加载相比,在两种情况下铁剥夺都产生相反的效果。这些观察结果表明,TfR2的表达可能在人类癌症中发生改变,值得在原发性肿瘤中进行进一步研究。此外,我们的研究表明,至少在肿瘤细胞中,TfR2的表达通过不同的生化机制受铁调节,其分子基础仍有待确定。