Polysplenia syndrome: a case with congenital heart block, infarction of a splenic mass, and a short pancreas.
作者信息
Sriplung H
机构信息
Department of Pathology, Faculty of Medicine, Prince of Songkla University, Thailand.
出版信息
J Med Assoc Thai. 1991 Jun;74(6):355-8.
PMID:1744542
Abstract
A case of polysplenia with congenital heart block, infarction of a splenic mass, and a short pancreas was reported. The infant died of severe heart failure at the age of 28 days. Deformity of the SA node was suspected to be the cause of congenital heart block but could not be demonstrated because of some limitations of autopsy procedure. Redundant splenic pedicle might cause infarction of a splenic mass after birth. The author suggests that, in addition to the semi-annular pancreas, the pancreatic anomalies of this syndrome should include the short pancreas.
摘要
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