气管支气管巨大症合并间质性肺纤维化。

Tracheobronchomegaly associated with interstitial pulmonary fibrosis.

作者信息

Vidal C, Peña F, Rodríguez Mosquera M, González Quintela A

机构信息

Clínica Puerta de Hierro, Madrid, Spain.

出版信息

Respiration. 1991;58(3-4):207-10. doi: 10.1159/000195928.

DOI:10.1159/000195928

PMID:1745857

Abstract

Tracheobronchomegaly (TBM) is the syndrome of enlarged trachea and main bronchi associated with recurrent and chronic respiratory tract infections. A 42-year-old man with TBM and diffuse interstitial pulmonary fibrosis is described. The possible relationship between the two entities is discussed and the etiology, pathogenesis, clinical manifestations, prognosis and treatment of TBM are reviewed.

摘要

气管支气管巨大症（TBM）是一种与反复慢性呼吸道感染相关的气管和主支气管扩张综合征。本文描述了一名患有气管支气管巨大症和弥漫性间质性肺纤维化的42岁男性。讨论了这两种疾病之间可能的关系，并对气管支气管巨大症的病因、发病机制、临床表现、预后及治疗进行了综述。