He Jintian, Zhou Jialin, Wen Ruijin, Luo Renzhong
Department of Otolaryngology, Dongguan People's Hospital, Dongguan, 523000, China.
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2007 Feb;21(4):149-50, 153.
To explore the clinical and audiological characteristics of children with congenital malformations of the external ear.
One hundred and ten patients with congenital malformations of the external ear ranged from 2002 to 2006 were involved in this study. The mean age was one year and four months. The children were divided into three groups according to the appearance of the external ear. The first group consisted of 94 patients with auricle malformation and atresia of the external auditory meatus. The second group consisted of 8 patients with abnormal external auditory meatus (no atresia) and auricle malformation. The other 8 patients only with auricle malformation were included in the third group. All children underwent ABR tests, while some of these children accepted DPOAE and Acoustic-immittance measurements.
(1) Severe abnormal results of ABR were observed in 79 abnormal ears (78.22%) in children of first group, while moderate or severe abnormal results of ABR were observed only in 8 opposite side ears (normal ears). (2) Sixty-two and a half percent (5 ears) of ears of the second group (8 ears) had severely abnormal ABR results. (3) Severe abnormal ABR results occurred in 44.44 percent (4 ears) of ears of the third group (9 ears). Moderate or severe abnormal results of ABR were not observed in the opposite side ears (normal ears) in second and third groups.
Congenital malformations of the external ear is an important factor affecting children's hearing. Auditory nerve impairment can be observed in children with congenital malformations of the external ear.
探讨先天性外耳畸形患儿的临床及听力学特征。
本研究纳入了2002年至2006年间的110例先天性外耳畸形患者。平均年龄为1岁4个月。根据外耳外观将患儿分为三组。第一组包括94例耳廓畸形并外耳道闭锁的患者。第二组包括8例外耳道异常（无闭锁）并耳廓畸形的患者。第三组包括另外8例仅耳廓畸形的患者。所有患儿均接受了听性脑干反应（ABR）测试，其中部分患儿还接受了畸变产物耳声发射（DPOAE）及声导抗测量。
（1）第一组患儿中79只异常耳（78.22%）的ABR结果严重异常，而仅8只对侧耳（正常耳）的ABR结果为中度或重度异常。（2）第二组8只耳中有62.5%（5只耳）的ABR结果严重异常。（3）第三组9只耳中有44.44%（4只耳）的ABR结果严重异常。第二组和第三组的对侧耳（正常耳）未观察到ABR结果中度或重度异常。
先天性外耳畸形是影响儿童听力的重要因素。先天性外耳畸形患儿可出现听神经损害。
