Madill Karen E, Brammar Robin, Leatherbarrow Brian
Manchester Royal Eye Hospital, Manchester, United Kingdom.
Ophthalmic Plast Reconstr Surg. 2007 May-Jun;23(3):227-8. doi: 10.1097/IOP.0b013e31805593f1.
A 12-year-old girl with neurofibromatosis type 1 underwent subtotal anterior exenteration of a blind, unsightly, buphthalmic eye and orbital/eyelid plexiform neurofibroma. Simultaneously, a channeled Medpor orbital implant was positioned to reduce a meningoencephalocele resulting from severe sphenoid wing dysgenesis. Two-stage osseointegration was subsequently performed to permit secure fitting of an orbital prosthesis. This patient's cosmesis and social interaction were improved markedly with this surgical approach for disfiguring ocular, eyelid, and orbital disease due to neurofibromatosis type 1.
一名患有1型神经纤维瘤病的12岁女孩接受了对一只失明、外观不佳的牛眼及眼眶/眼睑丛状神经纤维瘤的前路次全切除术。同时，放置了带通道的Medpor眼眶植入物，以减轻因严重蝶骨翼发育不全导致的脑膜脑膨出。随后进行了两阶段骨整合，以确保眼眶假体的牢固安装。对于因1型神经纤维瘤病导致的毁容性眼部、眼睑和眼眶疾病，这种手术方法显著改善了该患者的外貌和社交互动。
