Peinado Rafael, Gnoatto Mariana, Merino Jose Luis, Oliver José María
Arrhythmia Unit, Department of Cardiology, Hospital Universitario La Paz, Universidad Autónoma, Paseo de la Castellana 261, 28046, Madrid, Spain.
Europace. 2007 Sep;9(9):848-50. doi: 10.1093/europace/eum077. Epub 2007 May 22.
An increased incidence of Wolff-Parkinson-White (WPW) syndrome with tricuspid atresia has been reported. Although atrioventricular accessory pathways may develop across suture lines after the Fontan-Björk procedure, the presence of multiple acquired accessory pathways has only been described rarely. We report on a case of a female with tricuspid atresia who underwent the Fontan operation at 5 years of age. One year later, she developed a WPW pattern. Narrow complex tachycardias started at the age of 18. An electrophysiological study revealed the presence of three accessory pathway connections at the surgical anastomosis level. All of them were successfully ablated and there were no recurrences.
据报道，三尖瓣闭锁合并预激综合征（WPW）的发病率有所增加。虽然在Fontan-Björk手术后，房室旁路可能会在缝合线处形成，但多条后天性旁路的存在仅在极少数情况下被描述过。我们报告了一例三尖瓣闭锁的女性患者，她在5岁时接受了Fontan手术。一年后，她出现了WPW图形。18岁时开始出现窄QRS波心动过速。电生理研究显示在手术吻合部位存在三条旁路连接。所有旁路均成功消融，且无复发。
