左房三房心：台湾地区的手术经验

Cor triatriatum sinistrum: surgical experience in Taiwan.

作者信息

Huang Yao-Kuang, Chu Jaw-Ji, Chang Jen-Ping, Lu Ming-Shian, Tseng Chi-Nan, Chang Yu-Sheng, Tsai Feng-Chun, Lin Pyng Jing

机构信息

Division of Thoracic and Cardiovascular Surgery, Chang Gung Memorial Hospital, Linko, Kaohsiung and Chia-Yi Center, Chang Gung University of Medicine, 5 Fu-Hsing Street, Kweishan, Taoyuan, 333, Taiwan.

出版信息

Surg Today. 2007;37(6):449-54. doi: 10.1007/s00595-006-3341-3. Epub 2007 May 28.

DOI:10.1007/s00595-006-3341-3

PMID:17522760

Abstract

PURPOSE

Cor triatriatum sinister, more commonly referred to as cor triatriatum (CT), is characterized by a common pulmonary venous chamber (proximal chamber) separated from the left atrium (distal chamber) by a fibromuscular septum. This report of our experience updates the surgical results of this anomaly in the Asian population.

METHODS

Between January 1992 and May 2005, nine patients with cor triatriatum underwent surgical correction at Chang Gung Memorial Hospital. We retrospectively analyzed their cardiac anatomy, clinical data, surgical procedures and follow-up data.

RESULTS

The mean age at surgery was 260+/-215 days (range, 20-790 days), with the exception of one patient who underwent surgery at 31 years of age. Three patients had a partial anomalous pulmonary venous connection, one had a complete atrioventricular canal defect, and one had another major complex cardiac anomaly. Eight corrective operations and one palliative operation were performed. There was no surgical mortality. The mean follow-up time was 52.1+/-43.6 months (range, 17-139 months).

CONCLUSION

Our findings show that surgical correction is efficient and safe for this rare cardiac anomaly.

摘要

目的

左房三房心，更常被称为三房心（CT），其特征是一个共同的肺静脉腔（近端腔）被一个纤维肌性隔膜与左心房（远端腔）分隔开。本报告介绍我们的经验，更新亚洲人群中这种异常情况的手术结果。

方法

1992年1月至2005年5月期间，9例三房心患者在长庚纪念医院接受了手术矫正。我们回顾性分析了他们的心脏解剖结构、临床资料、手术过程和随访数据。

结果

手术时的平均年龄为260±215天（范围为20 - 790天），但有1例患者在31岁时接受了手术。3例患者存在部分性肺静脉异位连接，1例有完全性房室管缺损，1例有另一种复杂的严重心脏畸形。共进行了8例矫正手术和1例姑息手术。无手术死亡病例。平均随访时间为52.1±43.6个月（范围为17 - 139个月）。