Nakajima Jun, Morota Tetsuro, Matsumoto Jun, Takazawa Yutaka, Murakawa Tomohiro, Fukami Takeshi, Yamamoto Tetsufumi, Takamoto Shinichi
Department of Cardiothoracic Surgery and Human Pathology, The University of Tokyo Graduate School of Medicine, and Department of Surgery, Asahi General Hospital, Tokyo, 113-8655, Japan.
Surg Today. 2007;37(6):496-9. doi: 10.1007/s00595-006-3432-1. Epub 2007 May 28.
Intimal sarcoma of the pulmonary artery is a rare disease. This neoplasm was characterized by an aggressive extension to the lumen of the pulmonary artery, thus mimicking a pulmonary thromboembolism. We herein report a 44-year-old woman who was diagnosed as having primary intimal sarcoma of the left lung preoperatively by transbronchial biopsy. The tumor originated in the pulmonary artery in the left lung, extending to the main pulmonary trunk via the pulmonary arterial lumen, thus resulting in stenosis of the main pulmonary trunk. A complete resection of the tumor with the left pneumonectomy and the pulmonary arterioplasty was successfully performed under cardiopulmonary bypass with vacuum assisted venous drainage.
肺动脉内膜肉瘤是一种罕见疾病。该肿瘤的特点是向肺动脉管腔侵袭性扩展，从而酷似肺血栓栓塞症。我们在此报告一名44岁女性，术前经支气管活检被诊断为左肺原发性内膜肉瘤。肿瘤起源于左肺的肺动脉，经肺动脉管腔延伸至主肺动脉干，导致主肺动脉干狭窄。在采用真空辅助静脉引流的体外循环下，成功实施了肿瘤完整切除并左肺切除术及肺动脉成形术。
