Arima-Iwasa Satomi, Chijiiwa Kazuo, Makino Ichiro, Tanabe Reiko, Ohuchida Jiro, Kondo Kazuhiro
Department of Surgery 1, Miyazaki University School of Medicine, Miyazaki, Japan.
Hepatogastroenterology. 2007 Mar;54(74):533-5.
Hepatic angiosarcoma is a non-epithelial malignant tumor and a rare primary neoplasm accounting for only a 0.1% of primary liver malignant tumors. Hepatic angiosarcoma progresses rapidly; therefore, most cases are discovered at an advanced stage, and less than 20% of the patients have received surgery. The lack of specific symptoms and radiological findings leads to the delay of diagnosis resulting in the poor prognosis. To the best of our knowledge, only three patients have been reported to survive for more than one year after hepatic resection for angiosarcoma. We herein report a patient with hepatic angiosarcoma, 4 cm in size, who underwent hepatic resection after confirming the diagnosis as angiosarcoma by the intraoperative frozen section examination. The patient is still alive for more than 16 months postoperatively without any signs of recurrence.
肝血管肉瘤是一种非上皮性恶性肿瘤,是一种罕见的原发性肿瘤,仅占原发性肝脏恶性肿瘤的0.1%。肝血管肉瘤进展迅速;因此,大多数病例在晚期才被发现,不到20%的患者接受了手术。缺乏特异性症状和影像学表现导致诊断延迟,从而预后较差。据我们所知,仅有3例患者在肝血管肉瘤肝切除术后存活超过1年。我们在此报告1例大小为4 cm的肝血管肉瘤患者,该患者经术中冰冻切片检查确诊为血管肉瘤后接受了肝切除术。患者术后已存活超过16个月,无任何复发迹象。