Nishi K, Yamada M, Morishita D, Nakamura Y, Murata Y, Fujioka M, Muramoto S, Murakami S, Seki M, Yasui M
Division of Internal Medicine, Noto General Hospital, Nanao.
Nihon Kyobu Shikkan Gakkai Zasshi. 1991 Aug;29(8):1042-6.
Leiomyosarcoma of the esophagus is a rare neoplasm. We reported a very rare case of esophageal leiomyosarcoma associated with pulmonary edema by the compression of the left atrium. A 67-year-old man was admitted with a 3-month history of chest pain, exertional dyspnea and dysphagia. Chest X-ray computed tomography showed posterior mediastinal tumor. Esophageogastroscopy and fiberoptic bronchofiberscopy showed no direct invasion of the tumor. By echocardiography, the left atrium was found to be compressed by the tumor and pulmonary hypertension (58/25 mmHg) and increased pulmonary wedge pressure (25 mmHg) was present. Open biopsy specimen demonstrated elongated cells suggestive of sarcoma. At autopsy, the tumor was confirmed to be leiomyosarcoma and to be originated from the lower esophagus.
食管平滑肌肉瘤是一种罕见的肿瘤。我们报告了一例非常罕见的食管平滑肌肉瘤,该肿瘤因压迫左心房而导致肺水肿。一名67岁男性因胸痛、劳力性呼吸困难和吞咽困难3个月入院。胸部X线计算机断层扫描显示后纵隔肿瘤。食管胃镜检查和纤维支气管镜检查未发现肿瘤有直接侵犯。通过超声心动图检查,发现左心房被肿瘤压迫,存在肺动脉高压(58/25 mmHg)和肺楔压升高(25 mmHg)。开放活检标本显示细胞呈细长形,提示为肉瘤。尸检时,肿瘤被确诊为平滑肌肉瘤,起源于食管下段。