Mazzocchi Octavio, Risso Jorge A, Viozzi Florencia, Apa Natalia P, Peralba Marina C, Nadal Miguel A, De Rosa Graciela E
5 Cátedra, Departamento de Medicina, Hospital de Clínicas José de San Martin, Facultad de Medicina, Universidad de Buenos Aires.
Medicina (B Aires). 2007;67(2):151-5.
Hypertrophic pachymeningitis is a very unusual disease, the main characteristic of which is thickening of the dura mater. We describe a patient who started this illness showing chronic headache and pauciimmune necrotizing extracapillary perinuclear antineutrophil cytoplasmic antibody (P-ANCA) associated glomerulonephritis. The diagnosis was made by brain magnetic resonance image. She received immunosuppressant therapy with prednisonel and cyclophosphamide with clinical improvement.
肥厚性硬脑膜炎是一种非常罕见的疾病,其主要特征是硬脑膜增厚。我们描述了一名患者,该患者以慢性头痛和寡免疫坏死性毛细血管外核周抗中性粒细胞胞浆抗体(P-ANCA)相关性肾小球肾炎起病。诊断通过脑部磁共振成像做出。她接受了泼尼松和环磷酰胺的免疫抑制治疗,临床症状有所改善。