Yalta Kenan, Turgut Okan Onur, Yilmaz Ahmet, Yilmaz Mehmet Birhan, Manduz Sinasi, Karadas Filiz, Dogan Kasim, Tandogan Izzet
Department of Cardiology, Cumhuriyet University, Sivas, Turkey.
Heart Surg Forum. 2007;10(3):E211-2. doi: 10.1532/HSF98.20071016.
Total anomalous pulmonary venous connection is an uncommon congenital anomaly in which all pulmonary venous return drains to the right atrium or one of its tributaries. Survival beyond infancy without surgical palliation is unlikely, so this anomaly is not encountered in the adult population with congenital heart disease. The patient presented here was 22 years old on admission and had no total anomalous pulmonary venous connection-associated symptoms. He underwent transthoracic echocardiographic examination for atypical chest pain. Transthoracic echocardiography along with cardiac catheterization favored the presence of a total anomalous pulmonary venous connection. Surgical correction of pulmonary venous confluence (draining to both the coronary sinus and right atrium) was performed successfully. This is a rare case of total anomalous pulmonary venous connection with no reported symptoms in contrast to the majority of patients who are symptomatic during the first year of life.
完全性肺静脉异位连接是一种罕见的先天性畸形,其中所有肺静脉回流均引流至右心房或其一个分支。未经手术姑息治疗而存活至婴儿期以后的情况不太可能发生,因此在患有先天性心脏病的成年人群中不会遇到这种畸形。此处介绍的患者入院时22岁,没有完全性肺静脉异位连接相关症状。他因非典型胸痛接受了经胸超声心动图检查。经胸超声心动图以及心导管检查支持存在完全性肺静脉异位连接。成功进行了肺静脉汇合(引流至冠状窦和右心房)的手术矫正。这是一例罕见的完全性肺静脉异位连接病例,与大多数在生命第一年就出现症状的患者不同,该患者没有症状报告。