Pratap Akshay, Saha Gauri Shankar, Bhattarai Bal Krishna, Yadav Rohit Prasad, Nepal Ajit, Bajracharya Amir, Kumar Anand, Adhikary Shailesh
Department of Surgery, B.P. Koirala Institute of Health Sciences, Dharan, Nepal.
J Pediatr Surg. 2007 Jul;42(7):1284-7. doi: 10.1016/j.jpedsurg.2007.02.032.
Tracheal agenesis is an extremely rare, typically fatal congenital tracheal malformation. Lack of prenatal symptoms and emergent presentation usually lead to a failure to arrive at the correct diagnosis and manage the airway properly before the onset of irreversible cerebral anoxia. We report the case history of an infant born with immediate respiratory failure who was diagnosed with tracheal agenesis. The clinical presentation, embryology, classification, and surgical management are discussed.
气管闭锁是一种极其罕见的、通常致命的先天性气管畸形。缺乏产前症状且病情紧急往往导致在不可逆的脑缺氧发作之前无法做出正确诊断并妥善处理气道。我们报告了一名出生时即出现呼吸衰竭并被诊断为气管闭锁的婴儿的病史。并对其临床表现、胚胎学、分类及手术治疗进行了讨论。
