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An inguinal hernia that was not meant to be: a female with seminoma.

作者信息

Costopoulos C, Ariyarathenam A V, Bullock N

机构信息

Department of Urology, Addenbrooke's Hospital, Queens' College, Cambridge CB3 9ET, UK.

出版信息

Hernia. 2008 Feb;12(1):99-101. doi: 10.1007/s10029-007-0247-y. Epub 2007 Jul 10.

DOI:10.1007/s10029-007-0247-y
PMID:17619944
Abstract

Complete androgen insensitivity is a rare X-linked disorder characterised by a female phenotype in a chromosomally male individual. It usually presents at puberty with primary amenorrhoea or as an inguinal mass in a female infant. Treatment includes bilateral orchidectomy and hormone replacement therapy. We present the case of a 31-year-old female with complete androgen insensitivity and a presumed inguinal hernia. We discuss the importance of early diagnosis, emphasise the consequences of misdiagnosis, and raise the question of whether such patients have been appropriately managed in the past.

摘要

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引用本文的文献

1
Complete androgen insensitivity syndrome with concomitant seminoma and Sertoli cell adenoma: an unusual combination.完全性雄激素不敏感综合征合并精原细胞瘤和支持细胞瘤:一种不寻常的组合。
BMJ Case Rep. 2016 Dec 30;2016:bcr2016217229. doi: 10.1136/bcr-2016-217229.

本文引用的文献

1
Testicular germ-cell cancer.睾丸生殖细胞癌
Lancet. 2006 Mar 4;367(9512):754-65. doi: 10.1016/S0140-6736(06)68305-0.
2
The syndrome of testicular feminization in male pseudohermaphrodites.男性假两性畸形中的睾丸女性化综合征。
Am J Obstet Gynecol. 1953 Jun;65(6):1192-1211. doi: 10.1016/0002-9378(53)90359-7.
3
Bilateral orchiectomy for the surgical treatment of complete androgen insensitivity syndrome: patient outcome after 1 year of follow-up.双侧睾丸切除术治疗完全性雄激素不敏感综合征:随访1年的患者结局
J Laparoendosc Adv Surg Tech A. 2003 Jun;13(3):193-7. doi: 10.1089/109264203766207735.
4
[Total androgenic insensitivity syndrome. Presentation as giant inguinal mass].[完全性雄激素不敏感综合征。表现为巨大腹股沟肿块]
Actas Urol Esp. 2001 Apr;25(4):303-6. doi: 10.1016/s0210-4806(01)72620-4.
5
Testicular feminization syndrome diagnosed in an elderly patient at surgery. A case report.老年患者手术中诊断出睾丸女性化综合征。病例报告。
Panminerva Med. 1996 Sep;38(3):193-8.
6
Inguinal hernias in females and the testicular feminization syndrome.女性腹股沟疝与睾丸女性化综合征
Am J Dis Child. 1969 Feb;117(2):243-51. doi: 10.1001/archpedi.1969.02100030245024.
7
Complete testicular feminisation syndrome in three sisters.三姐妹患完全性睾丸女性化综合征
Br J Urol. 1990 Mar;65(3):298-9. doi: 10.1111/j.1464-410x.1990.tb14733.x.
8
Testicular feminization: the androgen insensitivity syndrome.
J Pediatr Surg. 1992 Jun;27(6):757-60. doi: 10.1016/s0022-3468(05)80110-1.
9
Testicular feminization syndrome and associated gonadal tumors in Denmark.丹麦的睾丸女性化综合征及相关性腺肿瘤
Acta Obstet Gynecol Scand. 1992 Jan;71(1):63-6. doi: 10.3109/00016349209007950.