Gallego Javier, Mendes S, Roque J, Serpa C, Pereira R A, Mendes M, Lemos A, Nobre A, Cravino J
Serviço de Cirurgia Cardio-Torácica do Hospital de Santa Maria, Lisboa.
Rev Port Cir Cardiotorac Vasc. 2007 Apr-Jun;14(2):79-82.
The quadricuspid aortic valve is a rare aortic valve congenital malformation. The 2D transthoracic ultrasound (TTU) is not always effective in diagnosing quadricuspid aortic valves. The aim of this article is to present a case treated in our department, initially diagnosed as a mainly stenotic aortic valvular disease, while reviewing the clinical cases described so far. The authors report the case of a 74 year-old female patient with a mainly stenotic aortic valvular disease diagnosed by TTU. The only known risk factor was arterial hypertension. She underwent elective surgery in June 2005. The surgery consisted in replacing the quadricuspid aortic valve by a Carpentier Perimount no 21 Ao prosthesis. There were no post-operative complications. The patient revealed no symptoms in the post-operative 6 months and 1 year follow-up visits. The quadricupid aortic valve is a rare congenital malformation, with a considerable risk of serious complications. Patients with this diagnosis should be exhaustively studied. Medical literature describes some cases of quadricuspid aortic valve operated in other clinical centres. We present here the only case operated in our department in a 20-years period.
四叶式主动脉瓣是一种罕见的主动脉瓣先天性畸形。二维经胸超声心动图（TTU）对四叶式主动脉瓣的诊断并不总是有效的。本文旨在介绍我院治疗的一例病例，该病例最初被诊断为以主动脉瓣狭窄为主的疾病，同时回顾迄今为止所描述的临床病例。作者报告了一例74岁女性患者，经TTU诊断为以主动脉瓣狭窄为主的疾病。唯一已知的危险因素是动脉高血压。她于2005年6月接受了择期手术。手术内容是用21号Carpentier Perimount主动脉瓣假体替换四叶式主动脉瓣。术后无并发症。在术后6个月和1年的随访中，患者未出现任何症状。四叶式主动脉瓣是一种罕见的先天性畸形，有发生严重并发症的相当大风险。对于诊断为此病的患者应进行全面检查。医学文献描述了其他临床中心治疗的一些四叶式主动脉瓣病例。我们在此展示的是我院20年间唯一进行手术治疗的病例。
