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三名患有囊性纤维化的青少年出现严重肾病。

Severe nephropathy in three adolescents with cystic fibrosis.

作者信息

Melzi M L, Costantini D, Giani M, Appiani A C, Giunta A M

机构信息

Department of Paediatrics, University of Milan, Italy.

出版信息

Arch Dis Child. 1991 Dec;66(12):1444-7. doi: 10.1136/adc.66.12.1444.

DOI:10.1136/adc.66.12.1444
PMID:1776895
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1793375/
Abstract

Renal involvement has rarely been reported in patients with cystic fibrosis. We describe severe nephropathy with a rapidly fatal outcome in three adolescents with cystic fibrosis, and evaluate the important repercussions that the nephrotic syndrome had on the precarious clinical situation of these patients.

摘要

囊性纤维化患者中肾脏受累情况鲜有报道。我们描述了3例患有囊性纤维化的青少年出现严重肾病并迅速致死的病例，并评估了肾病综合征对这些患者不稳定临床状况的重要影响。

相似文献

1
Severe nephropathy in three adolescents with cystic fibrosis.三名患有囊性纤维化的青少年出现严重肾病。
Arch Dis Child. 1991 Dec;66(12):1444-7. doi: 10.1136/adc.66.12.1444.
2
Amyloidosis complicating cystic fibrosis.淀粉样变性并发囊性纤维化。
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Renal involvement in cystic fibrosis: diseases spectrum and clinical relevance.囊性纤维化的肾脏受累：疾病谱及临床相关性。
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Reactive amyloidosis.反应性淀粉样变性
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本文引用的文献

1
Circulating immune complexes containing IgA, IgG and IgM in patients with primary IgA nephropathy and with Henoch-Schoenlein nephritis. Correlation with clinical and histologic signs of activity.原发性IgA肾病和过敏性紫癜性肾炎患者循环中含IgA、IgG和IgM的免疫复合物。与临床及组织学活动征象的相关性。
Clin Nephrol. 1982 Nov;18(5):230-9.
2
The nephropathy of cystic fibrosis: a human model of chronic nephrotoxicity.囊性纤维化肾病：慢性肾毒性的人类模型
Hum Pathol. 1982 Oct;13(10):934-9. doi: 10.1016/s0046-8177(82)80056-7.
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Systemic amyloidosis in cystic fibrosis.
Acta Paediatr Scand. 1985 Jul;74(4):613-4. doi: 10.1111/j.1651-2227.1985.tb11043.x.
4
Glomerular deposition of immune complexes prepared with monomeric or polymeric IgA.用单体或聚合IgA制备的免疫复合物在肾小球的沉积。
Clin Exp Immunol. 1985 May;60(2):363-8.
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Microscopic nephrocalcinosis in cystic fibrosis.
N Engl J Med. 1988 Aug 4;319(5):263-6. doi: 10.1056/NEJM198808043190502.
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Systemic amyloidosis in cystic fibrosis.
Am J Dis Child. 1977 Aug;131(8):886-8. doi: 10.1001/archpedi.1977.02120210064013.