三名患有囊性纤维化的青少年出现严重肾病。
Severe nephropathy in three adolescents with cystic fibrosis.
作者信息
Melzi M L, Costantini D, Giani M, Appiani A C, Giunta A M
机构信息
Department of Paediatrics, University of Milan, Italy.
出版信息
Arch Dis Child. 1991 Dec;66(12):1444-7. doi: 10.1136/adc.66.12.1444.
Abstract
Renal involvement has rarely been reported in patients with cystic fibrosis. We describe severe nephropathy with a rapidly fatal outcome in three adolescents with cystic fibrosis, and evaluate the important repercussions that the nephrotic syndrome had on the precarious clinical situation of these patients.
摘要
囊性纤维化患者中肾脏受累情况鲜有报道。我们描述了3例患有囊性纤维化的青少年出现严重肾病并迅速致死的病例，并评估了肾病综合征对这些患者不稳定临床状况的重要影响。
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