Eren S
Department of Radiology, Faculty of Medicine, Atatürk University, Erzurum, Turkey.
Eur J Pediatr Surg. 2007 Aug;17(4):285-8. doi: 10.1055/s-2006-924376.
Desmoid tumours, also known as aggressive fibromatosis, are rare lesions with an intermediate biological behaviour between benign fibrous lesions and fibrosarcomas. Although abdominal desmoids have an increased incidence in Gardner's syndrome, they are rarely found in an isolated form. We report the findings of a barium study, ultrasound, computed tomography and magnetic resonance imaging in a nine-year-old boy with intermittent nausea and vomiting, diagnosed as having a desmoid tumour. Although intra-abdominal desmoids are usually detected as a solitary lesion in sporadic cases, the presented case had two mesenteric lesions in the left upper quadrant. There was intestinal obstruction and the masses had invaded the colon wall.
硬纤维瘤,也称为侵袭性纤维瘤病,是一种罕见的病变,其生物学行为介于良性纤维性病变和纤维肉瘤之间。尽管腹部硬纤维瘤在加德纳综合征中的发病率有所增加,但很少以孤立形式出现。我们报告了一名9岁男孩的钡剂造影、超声、计算机断层扫描和磁共振成像检查结果,该男孩有间歇性恶心和呕吐症状,被诊断为患有硬纤维瘤。虽然散发性病例中的腹腔内硬纤维瘤通常表现为单个病变,但本病例在上腹左象限有两个肠系膜病变。存在肠梗阻,且肿块侵犯了结肠壁。