Porru D, Stancati S, Giliberto G L, Gerardini M, Corinti M, Dionigi P, Rovereto B
Divisione Urologia, IRCCS Policlinico S. Matteo, Pavia, Italy.
Urology. 2004 Nov;64(5):1031. doi: 10.1016/j.urology.2004.06.022.
A 28-year-old man with Gardner syndrome was admitted to our Department because of multiple abdominal masses. Abdominal computed tomography revealed severe hydronephrosis of both kidneys due to ureteral compression against the pelvic bones exerted by multiple solid abdominal masses. The patient developed oligoanuria. Right percutaneous nephrostomy tube placement was followed by restoration of diuresis and progressive recovery of renal function of the left side. The patient then underwent median laparotomy and removal of five large desmoid tumors originating from the abdominal wall. Bilateral ureteral obstruction due to abdominal desmoid tumors can be a rare urologic complication of Gardner syndrome.
一名28岁的加德纳综合征患者因腹部出现多个肿块而入住我院。腹部计算机断层扫描显示，多个实性腹部肿块压迫盆腔骨，导致双侧肾脏严重肾积水。患者出现少尿和无尿。右侧经皮肾造瘘管置入后，尿量恢复，左侧肾功能逐渐恢复。随后，患者接受了正中剖腹手术，切除了起源于腹壁的5个大硬纤维瘤。腹部硬纤维瘤导致的双侧输尿管梗阻是加德纳综合征罕见的泌尿系统并发症。
